Language Profile of a Vietnamese Child with Prader-Willi Syndrome

Authors

  • Yen Nguyen

    Psychology and Education Department, Vietnam National Academy of Educational Management, Hanoi, Vietnam
  • Ben Phạm

    Faculty of Special Education, Hanoi National University of Education, Hanoi, Vietnam
  • Hang Phạm

    Research Center for General Education Development, Vietnam National Institute of Educational Sciences, Hanoi, Vietnam
  • Van Phạm

    VietSpeech EDU Early Intervention Center, Hanoi, Vietnam
  • Thu Dinh

    Faculty of Special Education, Hanoi National University of Education, Hanoi, Vietnam
  • Phuong Nguyen

    Faculty of Special Education, Hanoi National University of Education, Hanoi, Vietnam
  • Thanh Nguyen

    Psychology and Education Department, Vietnam National Academy of Educational Management, Hanoi, Vietnam

DOI:

https://doi.org/10.30564/fls.v6i5.6527
Received: 30 April 2024 | Revised: 14 August 2024 | Accepted: 9 September 2024 | Published Online: 15 November 2024

Abstract

Prader-Willi Syndrome (PWS), a low incidence genetic syndrome, exhibits complex difficulties characterized by infantile hypotonia and feeding, motor, cognition, behavioral phenotype, and hypoplasia. Children with PWS also may demonstrate delay in language development. However, this has not been well-investigated in research. To date, there is no research reporting the speech and language abilities of Vietnamese speaking population with PWS. This case report is the first attempt to describe the speech and language profile of a Vietnamese-speaking child with PWS. A 5-year-old boy with PWS participated in the study by completing speech and language tasks available in the Vietnamese language, including oral motor, speech accuracy, intelligibility, speech participation, receptive and expressive vocabulary, sentence repetition, rapid naming, phonological awareness skills, nonword repetition and telling and retelling stories. The performances of the majority of the tasks were digitally audio-recorded, then transcribed for speech and language analysis. The tasks’ scores were calculated then compared to the corresponding results available for typically developing same-aged peers and those with speech and language disorders. The child’s scores demonstrated poor oral motor skills, severe impairment of speech accuracy, and low speech intelligibility and participation. Language skills were low in vocabulary, grammar and narrative skills. Despite some facial abnormalities, the child demonstrated normal vocal characteristics. This case report supports the fact that Vietnamese individuals with PWS may experience a delay in language development compared to typically developing peers, even though the individuals receive early intervention services; therefore, continually speech and language support the individuals in mainstream school is essential.

Keywords:

Case Report; Comprehensive Assessment; Assessment Protocol; Speech and Language; Vietnamese; Prader Willi

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How to Cite

Nguyen, Y., Phạm, B., Phạm, H., Phạm, V., Dinh, T., Nguyen, P., & Nguyen, T. (2024). Language Profile of a Vietnamese Child with Prader-Willi Syndrome. Forum for Linguistic Studies, 6(5), 809–821. https://doi.org/10.30564/fls.v6i5.6527

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Vol. 6 , Iss. 5 (November 2024)

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Copyright © 2024 Trinh Thi Ha, Nguyen Thi Thu Hien, Nguyen Thi An, Nguyen Thi Mai Huong

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